Unknown

A 12-year-old male presented with history of recurrent nose bleeds along with easy bruising with frequent formation of muscle hematomas and prolonged bleeding following tril trauma. On examination, ceain skin lesions were seen along with jaundice, splenomegaly, ahropathy, joint and skin laxity. Lab findings revealed, Normal PT Prolonged aPTT Reduced ristocetin cofactor activity Low factor VIII assay Normal platelet count and size Platelet granules are normal. What is the most probable diagnosis of the above condition: -