Which among the following is not seen in Sturge Weber syndrome?
**Core Concept**
Sturge Weber syndrome is a rare neurocutaneous disorder characterized by a congenital skin lesion, typically a port-wine stain, and associated neurological abnormalities. The condition involves the trigeminal nerve and its branches, leading to vascular malformations in the brain and eye.
**Why the Correct Answer is Right**
The correct answer is not directly related to the core features of Sturge Weber syndrome, which include:
- A port-wine stain (a type of birthmark)
- Leptomeningeal angioma (a vascular malformation in the brain)
- Glaucoma
- Seizures
- Intellectual disability
- Hemiparesis (weakness on one side of the body)
**Why Each Wrong Option is Incorrect**
**Option A:** Glaucoma is a common feature of Sturge Weber syndrome, often presenting in childhood. It is essential to monitor for glaucoma in patients with this condition.
**Option B:** Seizures are another hallmark of Sturge Weber syndrome, resulting from the leptomeningeal angioma affecting the brain. Seizure control is crucial in managing the condition.
**Option C:** Intellectual disability is a frequent consequence of Sturge Weber syndrome, often due to the associated leptomeningeal angioma and seizures.
**Clinical Pearl / High-Yield Fact**
The classic "tram-track" calcifications seen on radiographs are a distinctive feature of Sturge Weber syndrome, often appearing in the cerebral cortex along the distribution of the trigeminal nerve.
**Correct Answer: D.**