Unknown

A 6 year old boy is brought to pediatric OPD by his mother. She complains that the child keeps suffering from fractures after minor trauma. Multiple such episodes have been repoed. She also complains that child faces problem in hearing and often misses on her instructions. Examination revealed the following finding: With lower limb deformity. His x-ray of lower limb is done which is shown as follows: Which of the given option defect is responsible for above clinical scenario?