Pediatrics Which disorder of carbohydrate metabolism typically has cardiac involvement? A Glycogen Storage Disease Type I (Von Gierke disease) B Glycogen Storage Disease Type II (Pompe disease) C Hereditary fructose intolerance D Galactosemia π‘ Explanation Which disorder of carbohydrate metabolism typically has cardiac involvement? β Correct Answer: B. Glycogen Storage Disease Type II (Pompe disease)