True about histiocytosis X include the following EXCEPT
Correct Answer: Associated with angiomyolipoma of kidney
Description: Ans. d (Associated with angiolipoma of kidney). (Ref. Nelson Textbook of Pediatrics 17^/1728; TABLE 499-1)Eosinophilic Granuloma (EG)# EG usually occurs during the first 3 decades and is most common in boys 5-10 yr.# The skull is most commonly/ affected, but any bone may be involved.# Usually present with local pain and swelling. There is often tenderness and warmth in the area of bone.# Spinal lesions may cause pain, stiffness, and occasional neurologic symptoms.# X-ray: Lytic lesions have well-defined or irregular margins {geographic skull) with expansion of the bone.# Spine involvement may cause uniform compression or flattening of the vertebral body (vertebra plana).# No extraskeletal (visceral) involvement distinguishes EG from the other forms of Langerhans cell histiocytosis (Hand- Schiiller-Christian or Letterer-Siwe variants), which have a less favorable prognosis.# Treatment includes curettage and bone grafting, low-dose radiation therapy, or steroid injection.# Observation for symptomatic lesions is fine because most lesions heal spontaneously and do not recur.
Category:
Medicine
Get More
Subject Mock Tests
Practice with over 200,000 questions from various medical subjects and improve your knowledge.
Attempt a mock test nowMock Exam
Take an exam with 100 random questions selected from all subjects to test your knowledge.
Coming SoonGet More
Subject Mock Tests
Try practicing mock tests with over 200,000 questions from various medical subjects.
Attempt a mock test now