Pediatrics The metabolic defect in HEREDITARY FRUCTOSE INTOLERANCE is due to deficiency of enzyme: A Fructokinase B Aldolase-B C Xylitol dehydrogenase D Phosphofructokinase 💡 Explanation The metabolic defect in HEREDITARY FRUCTOSE INTOLERANCE is due to deficiency of enzyme: ✓ Correct Answer: B. Aldolase-B