Which of the following cyanotic hea diseases is associated with left axis of detion and left ventricular hyperophy?
**Core Concept**
Tetralogy of Fallot (TOF) is a congenital cyanotic heart disease characterized by four classic features: ventricular septal defect, pulmonary stenosis, right ventricular hypertrophy, and an overriding aorta. However, TOF is not associated with left axis deviation or left ventricular hypertrophy. The question is likely referring to a different cyanotic heart disease.
**Why the Correct Answer is Right**
The cyanotic heart disease associated with left axis deviation and left ventricular hypertrophy is Ebstein's anomaly. It is a rare congenital heart defect where the tricuspid valve is abnormally formed and the right ventricle is small. This leads to right atrial enlargement, left axis deviation due to the altered electrical conduction, and left ventricular hypertrophy due to the increased workload on the left ventricle.
**Why Each Wrong Option is Incorrect**
**Option A:** Tetralogy of Fallot (TOF) is characterized by right ventricular hypertrophy, not left ventricular hypertrophy.
**Option B:** Tricuspid atresia is a cyanotic heart disease, but it is not specifically associated with left axis deviation and left ventricular hypertrophy.
**Option C:** Transposition of the great arteries (TGA) is a cyanotic heart disease, but it is not typically associated with left axis deviation and left ventricular hypertrophy.
**Clinical Pearl / High-Yield Fact**
Ebstein's anomaly is often associated with a characteristic "boot-shaped" heart on chest X-ray due to the right ventricular hypoplasia.
**Correct Answer:** A. Ebstein's anomaly