Koenen’s periungal fibroma is seen in –
**Core Concept**
Koenen's periungual fibroma is a type of skin lesion associated with **tuberous sclerosis complex (TSC)**, a genetic disorder characterized by the growth of non-cancerous tumors in various parts of the body. The condition is also known as **Bourneville disease**. These fibromas are a key dermatological feature of TSC.
**Why the Correct Answer is Right**
The correct answer is associated with **tuberous sclerosis complex (TSC)**, which is a genetic disorder that causes non-malignant tumors to form in many different organs, including the skin. Koenen's periungual fibromas are a type of **angiofibroma** that appears as a small, firm, and usually painless growth around the fingernails or toenails.
**Why Each Wrong Option is Incorrect**
**Option A:** Not directly related to Koenen's periungual fibroma.
**Option B:** Incorrect, as it is not typically associated with this condition.
**Option C:** Not the correct answer, as Koenen's periungual fibroma is specifically linked to TSC.
**Clinical Pearl / High-Yield Fact**
Koenen's periungual fibromas are a significant diagnostic clue for **tuberous sclerosis complex (TSC)**, and their presence should prompt further evaluation for other signs of the disease, such as **ash leaf spots**, **shagreen patches**, and **renal angiomyolipomas**.
**Correct Answer:** D. Tuberous Sclerosis.