Biochemistry Isovaleric academia is caused by deficiency of – A Branched chain ketoacid dehydrogenase B Isovaleryl CoA decarboxylase C Isovaleryl CoA dehydrogenase D Isovaleryl CoA synthase π‘ Explanation Isovaleric academia is caused by deficiency of - β Correct Answer: C. Isovaleryl CoA dehydrogenase