All of the followings are true about Sprengel’s deformity, except:
**Core Concept**
Sprengel's deformity is a rare congenital anomaly characterized by the elevation and malformation of the scapula, resulting in a shortened and winged appearance. It is often associated with other congenital anomalies and syndromes.
**Why the Correct Answer is Right**
Sprengel's deformity is typically associated with other congenital anomalies, including Klippel-Feil syndrome, which involves the fusion of cervical vertebrae. This association is due to the shared embryological origin of the scapula and cervical spine. However, dextrocardia, or the abnormal positioning of the heart to the right side of the chest, is not a known association with Sprengel's deformity.
**Why Each Wrong Option is Incorrect**
**Option A:** Congenital scoliosis can be associated with Sprengel's deformity, as both conditions arise from abnormalities in vertebral development. The association is due to the shared embryological origin of the scapula and spine.
**Option B:** Diastematomyelia, a type of spina bifida, has been associated with Sprengel's deformity. The two conditions often occur together due to the shared embryological origin of the spine and scapula.
**Option C:** Klippel-Feil syndrome is indeed associated with Sprengel's deformity, as both conditions involve abnormalities in vertebral development. The two conditions often occur together due to the shared embryological origin of the spine and scapula.
**Clinical Pearl / High-Yield Fact**
Sprengel's deformity can be associated with other congenital anomalies, including Klippel-Feil syndrome, diastematomyelia, and congenital scoliosis. It is essential to recognize these associations to provide comprehensive care for patients with Sprengel's deformity.
**β Correct Answer: D. Associated with dextrocardia**