Exomphalos major should be operated at –
**Core Concept**
Exomphalos major is a congenital anomaly characterized by a protrusion of the intestines and other abdominal contents through a large umbilical hernia. The management of exomphalos major involves surgical repair to prevent complications such as intestinal obstruction and infection.
**Why the Correct Answer is Right**
The surgical repair of exomphalos major typically involves a staged approach, with the first stage being a primary repair of the abdominal wall defect and the second stage being a delayed intestinal repair. This approach is recommended due to the high risk of intestinal atresias and other associated anomalies. The primary repair is usually performed within the first few days of life to prevent further complications and allow for the growth of the child.
**Why Each Wrong Option is Incorrect**
**Option A:** This option is incorrect as immediate repair is not recommended due to the high risk of complications such as intestinal atresias and other associated anomalies.
**Option B:** This option is incorrect as it does not take into account the staged approach recommended for exomphalos major repair.
**Option C:** This option is incorrect as it is too general and does not specify the timing or approach for exomphalos major repair.
**Clinical Pearl / High-Yield Fact**
Exomphalos major is often associated with other congenital anomalies, including omphalocele, intestinal atresias, and cardiac defects. A thorough preoperative evaluation is essential to identify these associated anomalies and plan for their management.
**Correct Answer:** B.