Biochemistry Enzyme deficient in maple syrup urine disease: A Branched chain alpha keto acid decarboxylase B Methionine adenosyl transferase C Fumarylacetoacetate hydrolase D Tyrosine aminotransferase 💡 Explanation Enzyme deficient in maple syrup urine disease: ✓ Correct Answer: A. Branched chain alpha keto acid decarboxylase