Maffucci syndrome is associated with which bone tumor?
## **Core Concept**
Maffucci syndrome is a rare genetic disorder characterized by the presence of multiple **enchondromas** (benign cartilage tumors) and **hemangiomas** (benign blood vessel tumors). It is associated with an increased risk of developing malignant tumors, particularly **chondrosarcoma**.
## **Why the Correct Answer is Right**
The correct answer, **enchondroma**, is directly related to Maffucci syndrome. Enchondromas are benign cartilage tumors that occur within the bone and are a hallmark of this syndrome. Individuals with Maffucci syndrome have a higher risk of their enchondromas transforming into **chondrosarcoma**, a malignant cartilage tumor.
## **Why Each Wrong Option is Incorrect**
- **Option A:** This option is incorrect because, although osteochondroma is a type of bone tumor, it is not specifically associated with Maffucci syndrome. Osteochondromas are more commonly linked to **multiple osteochondromas** or **hereditary multiple osteochondromas** (HMO).
- **Option B:** This option is incorrect as there's no commonly recognized bone tumor directly associated with Maffucci syndrome by this name in standard medical literature.
- **Option D:** This option is incorrect because, while **non-ossifying fibroma** is a type of benign bone lesion, it is not characteristically associated with Maffucci syndrome.
## **Clinical Pearl / High-Yield Fact**
A key clinical pearl is that patients with Maffucci syndrome require regular monitoring due to the risk of malignant transformation of enchondromas to **chondrosarcoma**. Early detection of such transformation can significantly impact management and prognosis.
## **Correct Answer:** . Enchondroma