Biochemistry The Refsum’s disease in which there is accumulation of phytanic acid is due to defect of A Carnitine palmitoyl transferase-I deficiency B HMG-CoA lyase deficiency C b-oxidation D a-oxidation π‘ Explanation The Refsum's disease in which there is accumulation of phytanic acid is due to defect of β Correct Answer: D. a-oxidation