D i.e. Chemotherapy and Radiation therapy It is the most common childhood primary orbital malignancy Q and also the m.c. soft tissue malignancy of childhood Q Clinical Presentation Treatment * It presents in 1' decade (.7 year) with rapidly progressive proptosis Q * Radiotherapy followed by chemotherapy Q with vincristine, actinomycin, & cyclosphosphamide * Swelling & injection of overlying skin; but the skin is not * Surgical excision is reserved for rare recurrent or warm. radioresistant tumors. * CT scan shows extraocular mass of homogenous density with bony destruction. * Patients with tumor localized to orbit have a 95% of cure rate.