A 7 year old girl from Bihar presented with three episodes of massive hematemesis and melena. There is no history of jaundice. On examination, she had a large spleen, non-palpable liver and mild ascites. Portal vein was not visualized on ultrasonography. Liver function tests were normal and endoscopy revealed esophageal varices. The most likely diagnosis is –
Correct Answer: Portal hypertension due to extrahepatic obstruction
Description: Differentiation between Extrahepatic and Hepatic / Post hepatic portal hypertension
Post sinusoidal and hepatic causes of portal hypertension will have
evidence of Liver parenchymal damage / deranged LFT (jaundice)
a dilated portal vein on ultrasonography
Extrahepatic presinusoidal obstruction will not have any effect on the Liver and hence there will be no evidence of hepatocellular damage.
No jaundice / No raised deranged LFT
Also non visualization of portal vein is a characteristic of portal vein thrombosis, an Extrahepatic cause.
Esophageal varices and splenomegaly are a manifestation of portal hypertension and will be present in all the above sites of obstruction.
Category:
Pediatrics
Get More
Subject Mock Tests
Practice with over 200,000 questions from various medical subjects and improve your knowledge.
Attempt a mock test nowMock Exam
Take an exam with 100 random questions selected from all subjects to test your knowledge.
Coming SoonGet More
Subject Mock Tests
Try practicing mock tests with over 200,000 questions from various medical subjects.
Attempt a mock test now