Potter sequence, or Potter syndrome, is a rare autosomal recessive trait and is associated with renal agenesis or hypoplasia. Altered facial characteristics include flattened nasal bridge, mandibular micrognathia, malformed low-set ears, etc. Absence or lack of proper development of the kidneys causes oligohydramnios, or possibly anhydramnios. Multicystic dysplastic kidney and polycystic kidney are usually secondary to Potter sequence and are therefore not the cause of Potter sequence or oligohydramnios. Wilms tumor is a relatively common renal tumor that presents in children; it is not associated with oligohydramnios and Potter sequence. Extrophy of the bladder is a congenital defect that exposes the posterior surface of the bladder on the exterior of the abdominal wall; there is no indication of this defect in the patient.