Splenectomy is not useful as a mode of treatment in which of the following conditions?
Correct Answer: Porphyria
Description: Splenectomy is the modality of treatment for hereditary spherocytosis, thalassemia & sickle cell anemia. Splenectomy is of little benefit in the treatment of porphyria. Porphyrias are metabolic disorders, resulting from deficiency of enzymes in the heme biosynthetic pathway. These enzyme deficiencies are inherited as autosomal dominant, autosomal recessive, or X-linked traits, with the exception of porphyria cutanea tarda (PCT), which is usually sporadic. Ref: Harrisons Internal Medicine, 18th Edition, Chapter 358; Williams Hematology, 8th Edition, Chapter 57
Category:
Medicine
Get More
Subject Mock Tests
Practice with over 200,000 questions from various medical subjects and improve your knowledge.
Attempt a mock test nowMock Exam
Take an exam with 100 random questions selected from all subjects to test your knowledge.
Coming SoonGet More
Subject Mock Tests
Try practicing mock tests with over 200,000 questions from various medical subjects.
Attempt a mock test now