All are features of Pompe’s disease except

Correct Answer: Hyperglycemia
Description: Type II(Pompe) disease results from lysosomal storage of glycogen in skeletal muscles,cardiac muscles, and central nervous system. There is progressive cardiomyopathy.ECG shows left axis deviation,short PR interval & large QRS.Heart failure with dyspnoea and cyanosis may occur.Skeletal muscles show hypotonia and marked weakness.The tongue is large & protruding.It is also characterised by hepatomegaly and hypoglycemia.
Category: Pediatrics
Share:

Get More
Subject Mock Tests

Practice with over 200,000 questions from various medical subjects and improve your knowledge.

Attempt a mock test now
Mock Exam

Take an exam with 100 random questions selected from all subjects to test your knowledge.

Coming Soon
Get More
Subject Mock Tests

Try practicing mock tests with over 200,000 questions from various medical subjects.

Attempt a mock test now
Mock Exam

Attempt an exam of 100 questions randomly chosen from all subjects.

Coming Soon
WordPress › Error

There has been a critical error on this website.

Learn more about troubleshooting WordPress.