Cystic medial necrosis responsible for aoic dilatation and rupture is seen in –
Correct Answer: Marfan syndrome
Description: Ans. is 'd' Marfan syndromeo Cystic medial necrosis is the degenerative disease of media of the aoa.o It characterized by degeneration of collagen and elastic fibers in tunica media of aoa, and also the loss of medial cells that are replaced by multiple cleft of mucoid material.It characteristically affects the proximal aoer, results in circumferential weakness and dilatation which results in the development offusiform aneurysm involving the ascending aoa and sinus of vulsalva.o Cystic medial necrosis is a pathological substrate for aoic dissection.Diseases causing cystic medial necrosis o Marfan syndromeo Ehler-Danlus syndrome (type IV)o Congenital bicuspid aoic valveo Familial thoracic aoic aneurysm syndrome o Pregnancy
Category:
Pathology
Get More
Subject Mock Tests
Practice with over 200,000 questions from various medical subjects and improve your knowledge.
Attempt a mock test nowMock Exam
Take an exam with 100 random questions selected from all subjects to test your knowledge.
Coming SoonGet More
Subject Mock Tests
Try practicing mock tests with over 200,000 questions from various medical subjects.
Attempt a mock test now