All of the following are Vitamin B6 dependent syndromes, EXCEPT:

Correct Answer: Darier disease
Description: Darier disease- autosomal dominant, characterized by greasy hyperkeratotic papules in seborrheic regions, nail abnormalities, and mucous membrane changes. Vitamin B6 dependence syndromes syndromes : pyridoxine-dependent epilepsy, a vitamin B6-responsive anemia, xanthurenic aciduria, cystathioninuria, and homocystinuria.
Category: Pediatrics
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